ABCD1 is an ATP-binding cassette transporter located on the peroxisomal membrane with specific structure and function. It utilizes the energy of ATP hydrolysis to transport ultra-long-chain fatty acids to peroxisomes for β-oxidation, maintaining intracellular lipid balance. The structural characteristics of ABCD1 include two nucleotide binding domains and two transmembrane domains, which undergo conformational changes during substrate binding to achieve substrate transport. However, when ABCD1 is dysfunctional, it can lead to abnormal accumulation of ultra-long-chain fatty acids in the cytosol, which can cause neurodegenerative diseases such as X-linked adrenoleukodystrophy.
Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1)-VLPs
CSB-MP001068HU
The following ABCD1 reagents supplied by CUSABIO are manufactured under a strict quality control system. Multiple applications have been validated and solid technical support is offered.
ABCD1 Antibodies for Homo sapiens (Human)
| Code | Product Name | Species Reactivity | Application |
|---|---|---|---|
| CSB-PA001068GA01HU | ABCD1 Antibody | Human,Mouse,Rat | ELISA,WB,IHC |
| CSB-PA214656 | ABCD1 Antibody | Human | ELISA,WB |
| CSB-PA008163 | ABCD1 Antibody | Human | WB, ELISA |
| CSB-PA001068LA01HU | ABCD1 Antibody | Human | ELISA, IHC |
ABCD1 Antibodies for Arabidopsis thaliana (Mouse-ear cress)
| Code | Product Name | Species Reactivity | Application |
|---|---|---|---|
| CSB-PA856736XA01DOA | ABCD1 Antibody | Arabidopsis thaliana | ELISA, WB (ensure identification of antigen) |
ABCD1 Proteins for Homo sapiens (Human)
| Code | Product Name | Source |
|---|---|---|
| CSB-CF001068HU | Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1) (Active) | in vitro E.coli expression system |
|
CSB-YP001068HU1 CSB-EP001068HU1 CSB-BP001068HU1 CSB-MP001068HU1 CSB-EP001068HU1-B |
Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1), partial |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
| CSB-MP001068HU | Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1)-VLPs | Mammalian cell |
ABCD1 Proteins for Mus musculus (Mouse)
| Code | Product Name | Source |
|---|---|---|
| CSB-CF001068MO | Recombinant Mouse ATP-binding cassette sub-family D member 1 (Abcd1) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
|
CSB-YP001068MO1 CSB-EP001068MO1 CSB-BP001068MO1 CSB-MP001068MO1 CSB-EP001068MO1-B |
Recombinant Mouse ATP-binding cassette sub-family D member 1 (Abcd1), partial |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ABCD1 Proteins for Dictyostelium discoideum (Slime mold)
| Code | Product Name | Source |
|---|---|---|
| CSB-CF690732DKK | Recombinant Dictyostelium discoideum ABC transporter D family member 1 (abcD1) |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
|
CSB-YP690732DKK1 CSB-EP690732DKK1 CSB-BP690732DKK1 CSB-MP690732DKK1 CSB-EP690732DKK1-B |
Recombinant Dictyostelium discoideum ABC transporter D family member 1 (abcD1), partial |
Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |